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CASE REPORT
Year : 2016  |  Volume : 7  |  Issue : 6  |  Page : 523-525

Encephalocraniocutaneous lipomatosis (Haberland syndrome): A rare case report


Department of Dermatology, B.J. Medical College, Civil Hospital, Ahmedabad, Gujarat, India

Correspondence Address:
Ashish Jagati
Department of Dermatology, B.J. Medical College, Civil Hospital, Ahmedabad, Gujarat
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/2229-5178.193901

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Haberland syndrome or Fishman syndrome also known as encephalocraniocutaneous lipomatosis (ECCL) is a rare, congenital neurocutaneous disorder. It is characterized by unilateral involvement of skin, eyes and central nervous system. We report the case of a 28-year-old woman who presented with soft lipomatous swelling over right temporal area with nonscarring alopecia of part of frontal and parietal region. The patient had a history of seizures and ipsilateral scleral dermoid. Computed tomography scan findings were suggestive of lipomas and calcification of falx. Magnetic resonance imaging showed right-sided hemi atrophy and two intracranial cysts. We report this case because of its rarity.


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