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LETTER TO THE EDITOR
Year : 2017  |  Volume : 8  |  Issue : 3  |  Page : 225-226  

Sturge–Weber syndrome with choroidal hemangioma


1 Dr. Rajendra Prasad Centre for Ophthalmic Sciences, New Delhi, India
2 Department of Dermatology, KPC Medical College and Hospital, Jadavpur, Kolkata, West Bengal, India
3 Department of Dermatology and Venereology, All India Institute of Medical Sciences (AIIMS), New Delhi, India

Date of Web Publication11-May-2017

Correspondence Address:
Anupam Das
Department of Dermatology, KPC Medical College and Hospital, Kolkata - 700 032, West Bengal
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/idoj.IDOJ_148_16

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How to cite this article:
Tripathy K, Das A, Subhadarshani S. Sturge–Weber syndrome with choroidal hemangioma. Indian Dermatol Online J 2017;8:225-6

How to cite this URL:
Tripathy K, Das A, Subhadarshani S. Sturge–Weber syndrome with choroidal hemangioma. Indian Dermatol Online J [serial online] 2017 [cited 2019 Jul 21];8:225-6. Available from: http://www.idoj.in/text.asp?2017/8/3/225/206114

Sir,

A 13-year-old girl presented to the Department of Ophthalmology, with dimness of vision in the left eye. She had a port-wine stain on the face bilaterally, along with the involvement of left upper lid [Figure 1]. The left eye had an elevated round orange subretinal mass with ill-defined margins, suggestive of circumscribed choroidal hemangioma [Figure 2]. The left eye showed prominent red reflex due to the red color of the elevated hemangioma and induced hypermetropia. Intraocular pressure was raised in the left eye. She did not give a history of seizures. Based on the history and examination findings, a diagnosis of Sturge– Weber syndrome More Details (SWS) was made. She is presently being managed under a multidisciplinary approach for her ophthalmic condition and cutaneous lesion.
Figure 1: The color photograph of the face shows bilateral distribution of port-wine stain over the face and prominent red reflex in the left eye. The left pupil was pharmacologically dilated for better appreciation of the prominent red reflex

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Figure 2: The montage of color fundus photograph (Visucam 500, Carl Zeiss Meditec AG, Jena, Germany) of the left eye shows an elevated reddish subretinal mass with indistinct margin suggestive of a circumscribed choroidal hemangioma

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The manifestations of SWS include port-wine stain along the distribution of the trigeminal nerve, ipsilateral choroidal hemangioma, glaucoma, seizures, and leptomeningeal angioma.[1],[2] The choroidal hemangioma may be circumscribed or diffuse, and may be isolated or associated with SWS.[3] Treatment options for choroidal hemangioma causing vision loss include laser, photodynamic therapy, and radiotherapy.[3] In 15% of SWS (similar to our patient), port-wine stain may be bilateral.[2] Pulsed dye laser is the treatment of choice for port-wine stains.

Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

Financial support and sponsorship

Nil.

Conflicts of interest

There are no conflicts of interest.

 
   References Top

1.
Thomas-Sohl KA, Vaslow DF, Maria BL. Sturge-Weber syndrome: A review. Pediatr Neurol 2004;30:303-10.  Back to cited text no. 1
[PUBMED]    
2.
Piram M, Lorette G, Sirinelli D, Herbreteau D, Giraudeau B, Maruani A. Sturge-Weber syndrome in patients with facial port-wine stain. Pediatr Dermatol 2012;29:3-7.  Back to cited text no. 2
[PUBMED]    
3.
Tsipursky MS, Golchet PR, Jampol LM. Photodynamic therapy of choroidal hemangioma in Sturge-Weber syndrome, with a review of treatments for diffuse and circumscribed choroidal hemangiomas. Surv Ophthalmol 2011;56:68-85.  Back to cited text no. 3
[PUBMED]    


    Figures

  [Figure 1], [Figure 2]



 

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